To identify patients with advanced and rapidly progressive lung disease.
To discuss how to best optimise standard therapies.
To understand the different approaches appropriate to patients who have and have not decided that lung transplantation is an option.
To detail innovative strategies which may be worth attempting if conventional means failure.
Summary More than 90% of CF patients will eventually die of advanced lung disease, despite everything that has been attempted. This article will discuss strategies that can be adopted when a patient is doing badly.
- ©ERS 2005
Breathe articles are open access and distributed under the terms of the Creative Commons Attribution Non-Commercial Licence 4.0.