TY - JOUR T1 - GPs Meet Rare Lung Disorders Task Force factsheet: primary ciliary dyskinesia JF - Breathe JO - Breathe SP - 159 LP - 161 DO - 10.1183/20734735.112215 VL - 11 IS - 2 AU - Fernando M. de Benedictis Y1 - 2015/06/01 UR - http://breathe.ersjournals.com/content/11/2/159.abstract N2 - Primary ciliary dyskinesia (PCD) is a rare, autosomal recessive disease of abnormalities of ciliary structure and function. The result is impaired mucociliary clearance, causing a variety of respiratory symptoms, and likely progression to bronchiectasis in most cases. Situs anomalies are present in nearly 50% of cases. ER -