Abstract
The cystic lung diseases are rare orphan lung disorders that most physicians will see infrequently in their everyday practice. Diagnostic and treatment options have improved over recent decades, with opportunities for slowing rate of progression and improving outcome for patients. This review provides a summary of the clinical approach to these lung disorders, including how to differentiate between different imaging patterns, clinical features, differential diagnosis and characteristics of the commonest presenting disorders.
Educational aims
To understand the clinical, pathological and radiological features of cystic lung disorders
To explore the differential diagnosis of cystic lung disease
To be familiar with the key features (clinical, radiological, physiological and pathological) of the commoner cystic lung diseases, which assist in differentiating between these
Abstract
Cystic lung diseases are uncommon disorders with a wide differential diagnosis. Treatment has improved over the last decade and respiratory physicians should feel encouraged to investigate such cases thoroughly to reach a final diagnosis. https://bit.ly/2W6Is9D
Footnotes
Conflict of interest: S. Ennis has nothing to disclose.
Conflict of interest: E.J. Silverstone has nothing to disclose.
Conflict of interest: D.H. Yates has nothing to disclose.
- Received February 6, 2020.
- Accepted April 29, 2020.
- Copyright ©ERS 2020
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