RT Journal Article
SR Electronic
T1 State of the art: pulmonary hypertension
JF Breathe
JO Breathe
FD European Respiratory Society
SP 188
OP 197
DO 10.1183/20734735.001214
VO 10
IS 3
A1 Victor J. Samillan
A1 Andrew J. Peacock
YR 2014
UL http://breathe.ersjournals.com/content/10/3/188.abstract
AB Key points Pulmonary arterial hypertension is still a chronic and incurable disease The most common mutation found in familial pulmonary arterial hypertension is a defect in the bone morphogenetic protein receptor 2 gene Usually the final stage of the disease is right heart failure Educational aims To provide definitions and diagnostic methods for pulmonary hypertension To provide a general classification of pulmonary hypertension To provide an overview of the currently available treatments To provide a future vision of next-generation treatments