PT  - JOURNAL ARTICLE
AU  - Christopher J. Brereton
AU  - Helen E. Jo
TI  - Acute exacerbations of idiopathic pulmonary fibrosis and the role of corticosteroids
AID  - 10.1183/20734735.0086-2020
DP  - 2020 Sep 01
TA  - Breathe
PG  - 200086
VI  - 16
IP  - 3
4099  - http://breathe.ersjournals.com/content/16/3/200086.short
4100  - http://breathe.ersjournals.com/content/16/3/200086.full
SO  - Breathe2020 Sep 01; 16
AB  - An acute exacerbation of idiopathic pulmonary fibrosis (AEIPF) is a potentially fatal complication of an already debilitating disease. Management is currently centred on delivering excellent supportive care and identifying reversible triggers. Despite growing international awareness and collaboration, no effective therapies have been identified. Corticosteroids are often the mainstay of treatment; however, the evidence base for their use is poor. Here, we review our current understanding of the disease process and how to manage it, with a focus on the role of corticosteroid therapy.Acute exacerbations of IPF cause a rapid deterioration in respiratory status and are challenging to manage. With few other options, corticosteroids are widely used as standard of care; however. the evidence to support this is poor. https://bit.ly/3gvSokN