RT Journal Article
SR Electronic
T1 Holistic management of patients with progressive pulmonary fibrosis
JF Breathe
JO Breathe
FD European Respiratory Society
SP 230101
DO 10.1183/20734735.0101-2023
VO 19
IS 3
A1 Ana Oliveira
A1 Gaia Fabbri
A1 Thomas Gille
A1 Elena Bargagli
A1 Boris Duchemann
A1 Rachel Evans
A1 Hilary Pinnock
A1 Anne E. Holland
A1 Elisabetta Renzoni
A1 Magnus Ekström
A1 Steve Jones
A1 Marlies Wijsenbeek
A1 Anh Tuan Dinh-Xuan
A1 Guido Vagheggini
YR 2023
UL http://breathe.ersjournals.com/content/19/3/230101.abstract
AB Progressive pulmonary fibrosis (PF) is a complex interstitial lung disease that impacts substantially on patients' daily lives, requiring personalised and integrated care. We summarise the main needs of patients with PF and their caregivers, and suggest a supportive care approach. Individualised care, education, emotional and psychological support, specialised treatments, and better access to information and resources are necessary. Management should start at diagnosis, be tailored to the patient's needs, and consider end-of-life care. Pharmacological and non-pharmacological interventions should be individualised, including oxygen therapy and pulmonary rehabilitation, with digital healthcare utilised as appropriate. Further research is needed to address technical issues related to oxygen delivery and digital healthcare.Educational aimsTo identify the main needs of patients with PF and their caregivers.To describe the components of a comprehensive approach to a supportive care programme for patients with PF.To identify further areas of research to address technical issues related to the management of patients with PF.Patients with progressive PF need personalised care plans. Digital healthcare and pulmonary rehabilitation can provide support at every stage. Research is needed to solve technical issues with oxygen supplementation and improve patients' quality of life. https://bit.ly/44KnRc0