| Recurrent spontaneous nosebleeds Mucocutaneous telangiectases at characteristic sites (fingertips, lips and oral mucosa) Visceral AVMs (pulmonary, gastrointestinal, cerebral and hepatic) Family history of first-degree relative affected |
3–4 criteria: definite HHT; 2 criteria: possible HHT; 0–1 criterion: unlikely HHT.