Isolated pauci-immune pulmonary capillaritis# |
Systemic lupus erythematosus |
Granulomatosis with polyangiitis# |
Microscopic polyangiitis# |
Goodpasture’s syndrome |
Rheumatiod arthritis |
Polymyositis |
Primary antiphospholipid syndrome |
Scleroderma |
Idiopathic pauci-immune glomerulonephritis# |
Henoch–Schoenlein purpura |
Immunoglobulin A nephropathy |
Behçet’s syndrome |
Hypersensitivity vasculitis |
Eosinophilic granulomatosis with polyangiitis (Churg–Strauss)# |
Essential cryoglobulinaemia |
#: Antineutrophil cytoplasmic antibody-associated vasculitis