Table 3 Common causes of small vessel vasculitis of the lungs (pulmonary capillaritis)
Isolated pauci-immune pulmonary capillaritis#
Systemic lupus erythematosus
Granulomatosis with polyangiitis#
Microscopic polyangiitis#
Goodpasture’s syndrome
Rheumatiod arthritis
Polymyositis
Primary antiphospholipid syndrome
Scleroderma
Idiopathic pauci-immune glomerulonephritis#
Henoch–Schoenlein purpura
Immunoglobulin A nephropathy
Behçet’s syndrome
Hypersensitivity vasculitis
Eosinophilic granulomatosis with polyangiitis (Churg–Strauss)#
Essential cryoglobulinaemia
  • #: Antineutrophil cytoplasmic antibody-associated vasculitis