Table 8

Results of the questionnaire relating to rare lung diseases

Wrong responses
Which findings of imaging suggest CF?
 Wrong option: bilateral pleural effusion79%
 All other options: grading=05 (0–13)%
Which findings of imaging suggest PCD?
 Wrong option: biliary stones78%
 All other options: grading=00 (0–18)%
Which investigations should be undertaken to diagnose PCD?
 Wrong option: arterial blood gas analysis83%
 All other options: grading=05 (0–9)%
What are the main symptoms/signs/manifestations that could be suggestive of lung disease in a child with immunodeficiency?
 Wrong option: hyperhidrosis88%
 All other options: grading=00 (0–8)%
What are the main physical signs and findings that could be suggestive of lung disease due to immunodeficiency?
 Wrong option: normal physical examination70%
 All other options: grading=05 (0–22)%
  • Data are presented as median (min–max), unless otherwise stated. The percentage of wrong responses was calculated on valid responses (i.e. after missing and “I don’t know” responses were excluded) and is the sum of two contributions. Wrong option: responses were considered wrong when a grade >0 was attributed to the wrong option in the questionnaire. All other options: responses were considered wrong when a grade = 0 was attributed to the other options in the questionnaire. The summary figure is reported in terms of median (minimum–maximum) of the percentages of wrong responses to each option.