Table 1

Classification of childhood vasculitis

Predominantly large vessel vasculitis
 Takayasu arteritis
Predominantly medium sized vessel vasculitis
 Childhood polyarteritis nodosa
 Cutaneous polyarteritis
 Kawasaki disease
Predominantly small vessel vasculitis
 Granulomatous
  Granulomatosis with polyangiitis (GPA)
  Eosinophilic granulomatosis with polyangiitis (EGPA)
 Non-granulomatous
  Microscopic polyangiitis (MPA)
  Immunoglobulin A vasculitis (IgAV)
  Isolated cutaneous leukocytoclastic vasculitis
  Hypocomplementemic urticarial vasculitis (HUV)
Other vasculitis
 Behçet's disease
Vasculitis secondary to infection (including hepatitis B-associated polyarteritis nodosa), malignancies, and drugs, including hypersensitivity vasculitis
 Vasculitis associated with connective tissue diseases
 Isolated vasculitis of the central nervous system
 Cogan syndrome
 Unclassified

Reproduced from [4], with permission.