Predominantly large vessel vasculitis |
Takayasu arteritis |
Predominantly medium sized vessel vasculitis |
Childhood polyarteritis nodosa |
Cutaneous polyarteritis |
Kawasaki disease |
Predominantly small vessel vasculitis |
Granulomatous |
Granulomatosis with polyangiitis (GPA) |
Eosinophilic granulomatosis with polyangiitis (EGPA) |
Non-granulomatous |
Microscopic polyangiitis (MPA) |
Immunoglobulin A vasculitis (IgAV) |
Isolated cutaneous leukocytoclastic vasculitis |
Hypocomplementemic urticarial vasculitis (HUV) |
Other vasculitis |
Behçet's disease |
Vasculitis secondary to infection (including hepatitis B-associated polyarteritis nodosa), malignancies, and drugs, including hypersensitivity vasculitis |
Vasculitis associated with connective tissue diseases |
Isolated vasculitis of the central nervous system |
Cogan syndrome |
Unclassified |
Reproduced from [4], with permission.