TABLE 2

The 2022 American College of Rheumatology/European Alliance of Associations eosinophilic granulomatosis with polyangiitis classification criteria

Clinical criteriaObstructive airway disease+3
Nasal polyps+3
Mononeuritis multiplex+1
Laboratory criteriaBlood eosinophil count ≥1×109 cells per L+5
Biopsy evidence of extravascular eosinophilic inflammation+2
Positive test for cytoplasmic antineutrophilic cytoplasmic antibodies (cANCA) or anti-proteinase 3 (PR3) antibodies−3
Haematuria−1

Reproduced from [41] with permission.