Differential diagnoses of pulmonary renal syndrome
| ANCA-associated vasculitis | Granulomatosis with polyangiitis (GPA) |
| Microscopic polyangiitis (MPA) | |
| Eosinophilic granulomatosis with polyangiitis (EGPA) | |
| Anti-GBM disease | Anti-GBM disease |
| ANCA-negative vasculitis | IgA disease |
| Cryoglobulinaemia | |
| Drug-induced vasculitis | Cocaine |
| d-penicillamine | |
| Autoimmune connective tissue disease | Systemic lupus erythematosus (SLE) |
| Polymyositis | |
| Diabetes mellitus | |
| Mixed connective tissue disease (MCTD) | |
| Systemic sclerosis |
Classifying the differential diagnoses of pulmonary renal syndromes into groups based on the underlying pathological process. ANCA: anti-neutrophil cytoplasm antibodies; GBM: glomerular basement membrane.